LIBRO + ANEXOS NEUMOLOGÍA PEDIÁTRICA

Libro Blanco de las ACES Pediátricas 2024 136 ❚ a. Know which pneumonia-causing organisms are not associated with pleural effusions 4. Pulmonary function tests 5. Other investigations 6. Diagnostic criteria a. Know that chlamydial pneumonia is accompanied by eosinophilia 7. Complications e. Prevention and therapeutic approach 1. Prevention 2. Therapeutic approach 3. Side effects of therapy f. Prognosis 1. Natural history 2. Prognosis with therapy H. Disorders of the chest wall, diaphragm, and pleural space 1. Chest wall a. Ribs 1. Etiology/genetics a. Know that asphyxiating thoracic dystrophy is inherited in an autosomal recessive manner b. Recognize the inheritance and genetic mechanism underlying asphyxiating thoracic dystrophy c. Know that abnormalities of the ventral abdominal wall, eg, giant omphalocele, can result in a long thin chest wall and pulmonary hypoplasia 2. Pathophysiology a. Pathology b. Path mechanisms and consequences 1. Know that the chest wall abnormalities associated with asphyxiating thoracic dystrophy (short horizontal ribs and flared costochondral junctions) result in a fixed chest wall and hypoplastic lungs 2. Know the pathophysiologic consequences of chest wall restriction 3. Diagnosis and clinical manifestations a. History b. Physical examination 1. Recognize the association between a small, bell-shaped chest and chronically reduced rib excursion c. Imaging 1. Recognize the radiographic appearance of the rib cage characteristic of asphyxiating thoracic dystrophy 2. Recognize the radiographic appearance of abnormal thoracic vertebrae and ribs 3. Recognize the radiographic appearance of the chest characteristic of progressive spinal atrophy 4. Recognize the radiographic appearance of benign chest wall tumors d. Pulmonary function tests